CASE REPORT|Articles in Press

Undifferentiated Pleomorphic Sarcoma of the Thoracic Aorta: A Diagnostic and Therapeutic Challenge

Open AccessPublished:February 20, 2023DOI:
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      We describe the workup and treatment of a 52-year-old man presenting with an extensive primary tumor of the descending aorta. Workup prior to surgical resection suggested non-neoplastic etiologies for this lesion, and we detail the diagnostic and therapeutic challenge posed by these rare tumors.
      Primary tumors of the great vessels are exceedingly rare conditions typically characterized by late diagnosis and poor survival. Both the identification and treatment of these lesions can present significant challenges. We present the utilization of multiple imaging modalities to characterize an aortic lesion and its surgical resection. The patient has recovered uneventfully and is now undergoing adjuvant treatment.